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Su JW, Chua YL, Ong BH, Lim CH
Correspondence: Dr Jang Wen Su, email@example.com
Malignant peripheral nerve sheath tumour (MPNST) is a rare occurrence in the mediastinum. It is biologically aggressive and is generally resistant to chemoradiation therapy. The mainstay of treatment is complete surgical resection. We report a large MPNST which invaded into the adjacent aortic wall in a 50-year-old man. Extensive resection, which included aortic reconstruction under cardiopulmonary bypass and deep hypothermic arrest, was necessary for a good long-term outcome.
Keywords: aortic reconstruction, cardiopulmonary bypass, malignant mediastinal peripheral nerve sheath tumour, mediastinal nerve sheath tumour, phrenic nerve tumour
Singapore Med J 2009; 50(6): e199-e200